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1230062001: Congenital atresia of inferior vena cava without azygos continuation (disorder)


Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 30-Jun 2022. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
5067005011 Congenital atresia of inferior vena cava without azygos continuation (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
5067006012 Inferior vena cava interruption without azygos continuation en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
5067013012 Congenital atresia of inferior vena cava without azygos continuation en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
5400120013 A rare congenital anomaly of the inferior vena cava characterized by complete interruption of the vessel in which no direct continuity exists between the inferior vena cava and the azygos/hemiazygos system. Clinical manifestations depend on the variant drainage patterns or collaterals and include lower extremity deep vein thrombosis, thromboembolic attacks, leg swelling and pain, lower extremity varices, abdominal pain, intraabdominal varices, and hematochezia, among others. Additional venous abnormalities or cardiac malformations are frequently present. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
5400121012 A rare congenital anomaly of the inferior vena cava characterised by complete interruption of the vessel in which no direct continuity exists between the inferior vena cava and the azygos/hemiazygos system. Clinical manifestations depend on the variant drainage patterns or collaterals and include lower extremity deep vein thrombosis, thromboembolic attacks, leg swelling and pain, lower extremity varices, abdominal pain, intraabdominal varices, and haematochezia, among others. Additional venous abnormalities or cardiac malformations are frequently present. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core


0 descendants.

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Congenital atresia of inferior vena cava without azygos continuation (disorder) Is a Congenital atresia of inferior vena cava true Inferred relationship Some
Congenital atresia of inferior vena cava without azygos continuation (disorder) Occurrence Congenital true Inferred relationship Some 1
Congenital atresia of inferior vena cava without azygos continuation (disorder) Finding site Inferior vena cava structure true Inferred relationship Some 1
Congenital atresia of inferior vena cava without azygos continuation (disorder) Associated morphology Congenital atresia false Inferred relationship Some 1
Congenital atresia of inferior vena cava without azygos continuation (disorder) Pathological process (attribute) Pathological developmental process true Inferred relationship Some 1
Congenital atresia of inferior vena cava without azygos continuation (disorder) Associated morphology Atresia (morphologic abnormality) true Inferred relationship Some 1

Inbound Relationships Type Active Source Characteristic Refinability Group

Reference Sets

Component annotation with string value reference set (foundation metadata concept)

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