1228861004: Kaposiform lymphangiomatosis (disorder)

SNOMED CT Concept\Clinical finding (finding)\...

\Mass of body structure\Mass of soft tissue (finding)\Lymphangiomatosis (disorder)\Kaposiform lymphangiomatosis (disorder)

\General finding of soft tissue\Mass of soft tissue (finding)\Lymphangiomatosis (disorder)\Kaposiform lymphangiomatosis (disorder)
\General finding of soft tissue\Disorder of soft tissue\Lesion of soft tissue (disorder)\Lymphangiomatosis (disorder)\Kaposiform lymphangiomatosis (disorder)
\General finding of soft tissue\Disorder of soft tissue\Disorder of lymphatic vessel (disorder)\Lymphatic malformation\Lymphangiomatosis (disorder)\Kaposiform lymphangiomatosis (disorder)

\Disease\Disorder of foetus and/or newborn\Congenital disease (disorder)\Congenital malformation\Lymphatic malformation\Lymphangiomatosis (disorder)\Kaposiform lymphangiomatosis (disorder)
\Disease\Neoplasm and/or hamartoma (disorder)\Angiomatosis\Lymphangiomatosis (disorder)\Kaposiform lymphangiomatosis (disorder)
\Disease\Disorder of body system\Disorder of lymphatic system\Disorder of lymphatic vessel (disorder)\Lymphatic malformation\Lymphangiomatosis (disorder)\Kaposiform lymphangiomatosis (disorder)
\Disease\Disorder of soft tissue\Lesion of soft tissue (disorder)\Lymphangiomatosis (disorder)\Kaposiform lymphangiomatosis (disorder)
\Disease\Disorder of soft tissue\Disorder of lymphatic vessel (disorder)\Lymphatic malformation\Lymphangiomatosis (disorder)\Kaposiform lymphangiomatosis (disorder)
\Disease\Developmental disorder\Congenital malformation\Lymphatic malformation\Lymphangiomatosis (disorder)\Kaposiform lymphangiomatosis (disorder)

Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-May 2022. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module

5063491018 Kaposiform lymphangiomatosis (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core

5063492013 Kaposiform lymphangiomatosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core

5400048011 A rare vascular anomaly or angioma characterized by multifocal malformed lymphatic channels lined by clusters or sheets of spindled lymphatic endothelial cells with a predilection for the thoracic cavity, but also involving extra-thoracic locations, especially bones and spleen. Typical clinical signs and symptoms are pericardial and pleural effusions, cough, dyspnea, bleeding, and fractures secondary to bone involvement. Prognosis is generally poor due to the progressive nature of the condition. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core

5400049015 A rare vascular anomaly or angioma characterised by multifocal malformed lymphatic channels lined by clusters or sheets of spindled lymphatic endothelial cells with a predilection for the thoracic cavity, but also involving extra-thoracic locations, especially bones and spleen. Typical clinical signs and symptoms are pericardial and pleural effusions, cough, dyspnoea, bleeding, and fractures secondary to bone involvement. Prognosis is generally poor due to the progressive nature of the condition. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core

Expanded Value Set

Outbound Relationships	Type	Target	Active	Characteristic	Refinability	Group	Values
Kaposiform lymphangiomatosis (disorder)	Is a	Lymphangiomatosis (disorder)	true	Inferred relationship	Some
Kaposiform lymphangiomatosis (disorder)	Occurrence	Congenital	true	Inferred relationship	Some	1
Kaposiform lymphangiomatosis (disorder)	Finding site	Structure of lymphatic vessel	true	Inferred relationship	Some	1
Kaposiform lymphangiomatosis (disorder)	Associated morphology	Lymphangiomatosis	true	Inferred relationship	Some	1
Kaposiform lymphangiomatosis (disorder)	Pathological process (attribute)	Pathological developmental process	true	Inferred relationship	Some	1

Inbound Relationships

Type

Active

Source

Characteristic

Refinability

Group

Reference Sets

Component annotation with string value reference set (foundation metadata concept)

Back to Start

Id	Description	Lang	Type	Status	Case?	Module
5063491018	Kaposiform lymphangiomatosis (disorder)	en	Fully specified name	Active	Entire term case insensitive (core metadata concept)	SNOMED CT core
5063492013	Kaposiform lymphangiomatosis	en	Synonym (core metadata concept)	Active	Entire term case insensitive (core metadata concept)	SNOMED CT core
5400048011	A rare vascular anomaly or angioma characterized by multifocal malformed lymphatic channels lined by clusters or sheets of spindled lymphatic endothelial cells with a predilection for the thoracic cavity, but also involving extra-thoracic locations, especially bones and spleen. Typical clinical signs and symptoms are pericardial and pleural effusions, cough, dyspnea, bleeding, and fractures secondary to bone involvement. Prognosis is generally poor due to the progressive nature of the condition.	en	Definition	Active	Entire term case sensitive (core metadata concept)	SNOMED CT core
5400049015	A rare vascular anomaly or angioma characterised by multifocal malformed lymphatic channels lined by clusters or sheets of spindled lymphatic endothelial cells with a predilection for the thoracic cavity, but also involving extra-thoracic locations, especially bones and spleen. Typical clinical signs and symptoms are pericardial and pleural effusions, cough, dyspnoea, bleeding, and fractures secondary to bone involvement. Prognosis is generally poor due to the progressive nature of the condition.	en	Definition	Active	Entire term case sensitive (core metadata concept)	SNOMED CT core