| Inbound Relationships | Type | Active | Source | Characteristic | Refinability | Group | 
| Medullary cystic disease | Is a | False | Congenital cystic kidney disease | Inferred relationship | Existential restriction modifier |  | 
| Medullary sponge kidney | Is a | True | Congenital cystic kidney disease | Inferred relationship | Existential restriction modifier |  | 
| Fibrocystic kidney disease | Is a | False | Congenital cystic kidney disease | Inferred relationship | Existential restriction modifier |  | 
| Polycystic kidney disease, adult type | Is a | False | Congenital cystic kidney disease | Inferred relationship | Existential restriction modifier |  | 
| Polycystic kidney disease, infantile type | Is a | True | Congenital cystic kidney disease | Inferred relationship | Existential restriction modifier |  | 
| Microcystic renal disease | Is a | True | Congenital cystic kidney disease | Inferred relationship | Existential restriction modifier |  | 
| Simple renal cyst | Is a | False | Congenital cystic kidney disease | Inferred relationship | Existential restriction modifier |  | 
| Solitary multilocular renal cyst | Is a | True | Congenital cystic kidney disease | Inferred relationship | Existential restriction modifier |  | 
| Other specified congenital cystic kidney disease | Is a | False | Congenital cystic kidney disease | Inferred relationship | Existential restriction modifier |  | 
| [X]Other cystic kidney diseases | Is a | False | Congenital cystic kidney disease | Inferred relationship | Existential restriction modifier |  | 
| Family history: Polycystic kidney | Associated finding | False | Congenital cystic kidney disease | Inferred relationship | Existential restriction modifier | 1 | 
| Family history: Polycystic kidney | Associated finding | True | Congenital cystic kidney disease | Inferred relationship | Existential restriction modifier | 1 | 
| Family history: Polycystic kidney | Associated finding | False | Congenital cystic kidney disease | Inferred relationship | Existential restriction modifier | 1 | 
| Multinodular goiter, cystic kidney, polydactyly syndrome | Is a | False | Congenital cystic kidney disease | Inferred relationship | Existential restriction modifier |  | 
| Neonatal diabetes, congenital hypothyroidism, congenital glaucoma, hepatic fibrosis, polycystic kidney syndrome | Is a | True | Congenital cystic kidney disease | Inferred relationship | Existential restriction modifier |  | 
| Renal hepatic pancreatic dysplasia | Is a | True | Congenital cystic kidney disease | Inferred relationship | Existential restriction modifier |  | 
| Autosomal dominant polycystic kidney disease | Is a | True | Congenital cystic kidney disease | Inferred relationship | Existential restriction modifier |  | 
| Nephrocystin 3-related Meckel-like syndrome | Is a | True | Congenital cystic kidney disease | Inferred relationship | Existential restriction modifier |  | 
| Hepatic fibrosis, renal cyst, intellectual disability syndrome | Is a | True | Congenital cystic kidney disease | Inferred relationship | Existential restriction modifier |  | 
| Counseling for congenital polycystic kidney disease | Has focus | True | Congenital cystic kidney disease | Inferred relationship | Existential restriction modifier | 2 | 
| Cerebral ventriculomegaly, cystic kidney disease | Is a | True | Congenital cystic kidney disease | Inferred relationship | Existential restriction modifier |  | 
| [X]Other cystic kidney diseases | Is a | False | Congenital cystic kidney disease | Inferred relationship | Existential restriction modifier |  | 
| Other specified congenital cystic kidney disease | Is a | False | Congenital cystic kidney disease | Inferred relationship | Existential restriction modifier |  |