Status: current, Sufficiently defined by necessary conditions definition status. Date: 31-Jan 2002. Module: SNOMED CT core module
Descriptions:
| Id | Description | Lang | Type | Status | Case? | Module | 
| 133637014 | Spongy degeneration of central nervous system | en | Synonym | Active | Entire term case insensitive | SNOMED CT core module | 
| 133638016 | Cavanan-van Bogaert-Bertrand disease | en | Synonym | Inactive | Entire term case sensitive | SNOMED CT core module | 
| 133639012 | Spongy degeneration of white matter | en | Synonym | Active | Entire term case insensitive | SNOMED CT core module | 
| 133640014 | Canavan's disease | en | Synonym | Active | Entire term case sensitive | SNOMED CT core module | 
| 504449017 | Canavan-van-Bogaert-Bertrand disease | en | Synonym | Active | Entire term case sensitive | SNOMED CT core module | 
| 504450017 | Aspartoacylase deficiency | en | Synonym | Active | Entire term case insensitive | SNOMED CT core module | 
| 504451018 | Spongy degeneration of white matter in infancy | en | Synonym | Active | Entire term case insensitive | SNOMED CT core module | 
| 504452013 | Spongiform leucodystrophy | en | Synonym | Active | Entire term case insensitive | SNOMED CT core module | 
| 821716016 | Spongy degeneration of central nervous system (disorder) | en | Fully specified name | Active | Entire term case insensitive | SNOMED CT core module | 
| 2647269010 | Canavan-van Bogaert-Bertrand disease | en | Synonym | Active | Entire term case sensitive | SNOMED CT core module | 
| Inbound Relationships | Type | Active | Source | Characteristic | Refinability | Group | 
| Scrapie | Is a | False | Spongy degeneration of central nervous system | Inferred relationship | Existential restriction modifier | |
| Bovine spongiform encephalopathy | Is a | False | Spongy degeneration of central nervous system | Inferred relationship | Existential restriction modifier | |
| Jakob-Creutzfeldt disease | Is a | False | Spongy degeneration of central nervous system | Inferred relationship | Existential restriction modifier | |
| Kuru | Is a | False | Spongy degeneration of central nervous system | Inferred relationship | Existential restriction modifier | |
| Prion disease | Is a | False | Spongy degeneration of central nervous system | Inferred relationship | Existential restriction modifier | |
| Family history of spongy degeneration of central nervous system | Associated finding | True | Spongy degeneration of central nervous system | Inferred relationship | Existential restriction modifier | 1 | 
This concept is not in any reference sets