| Inbound Relationships | Type | Active | Source | Characteristic | Refinability | Group | 
| Ectodermal dysplasia with acanthosis nigricans syndrome | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Autosomal dominant palmoplantar keratoderma and congenital alopecia | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| X-linked intellectual disability with seizure and psoriasis syndrome | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Xeroderma pigmentosum and Cockayne syndrome complex | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Wooly hair and palmoplantar keratoderma with dilated cardiomyopathy syndrome | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Haim Munk syndrome | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Ankylosing vertebral hyperostosis with tylosis syndrome | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Diffuse palmoplantar keratoderma and acrocyanosis syndrome | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Psoriasis of anogenital region | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Intellectual disability, enteropathy, deafness, peripheral neuropathy, ichthyosis, keratoderma syndrome | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Cerebral dysgenesis, neuropathy, ichthyosis, palmoplantar keratoderma syndrome | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Palmoplantar keratoderma, 46,XX sex reversal, predisposition to squamous cell carcinoma syndrome | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Palmoplantar keratoderma with deafness syndrome | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Palmoplantar keratoderma Nagashima type | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Spastic paraplegia, intellectual disability, palmoplantar hyperkeratosis syndrome | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Keratosis follicularis, dwarfism, cerebral atrophy syndrome | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Trichodysplasia spinulosa caused by Polyomavirus | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Palmoplantar keratoderma with clinodactyly syndrome | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Hereditary skin peeling syndrome | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Arthrogryposis hyperkeratosis syndrome lethal form | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Van den Bosch syndrome | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Hyperkeratosis of mucous membrane of mouth due to and following traumatic injury | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Inverted follicular keratosis | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Disorder of keratinization | Is a | True | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Rough skin | Is a | True | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| [X]Other psoriasis | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| [X]Keratoderma in diseases classified elsewhere | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| [X]Other psoriatic arthropathies | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| [X]Hypertrophic disorder of skin, unspecified | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Acquired keratoderma NOS | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Psoriasis unspecified | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Other psoriasis and similar disorders | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Psoriasis and similar disorders NOS | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Psoriatic arthropathy NOS | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Other psoriasis | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Psoriasis NOS | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Hyperkeratosis NOS | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  | 
| Leukokeratosis | Has definitional manifestation | False | Abnormal keratinization | Inferred relationship | Existential restriction modifier |  |