| Inbound Relationships | Type | Active | Source | Characteristic | Refinability | Group | 
| Dandy-Walker syndrome | Is a | True | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Arnold-Chiari syndrome | Is a | False | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Congenital stenosis of aqueduct of Sylvius | Is a | False | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Spina bifida with hydrocephalus | Is a | True | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Foramen of Magendie atresia | Is a | False | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Foramen of Luschka atresia | Is a | False | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Congenital hydrocephalus caused by toxoplasmosis | Is a | False | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Other specified congenital hydrocephalus | Is a | False | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Congenital hydrocephalus NOS | Is a | False | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| [X]Other congenital hydrocephalus | Is a | False | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Myelocele with hydrocephalus | Is a | False | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Spina bifida with hydrocephalus of late onset | Is a | False | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Rachischisis with hydrocephalus | Is a | False | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Hydromyelocele with hydrocephalus | Is a | False | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Fetal hydrocephalus suspected | Associated finding | False | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier | 1 | 
| Cerebral degeneration due to congenital hydrocephalus | Due to | True | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier | 2 | 
| Fetal hydrocephalus suspected | Associated finding | False | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier | 1 | 
| Family history of congenital hydrocephalus | Associated finding | True | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier | 1 | 
| Agenesis of cerebellum and hydrocephalus syndrome | Is a | True | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Growth delay with hydrocephalus and lung hypoplasia syndrome | Is a | True | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Vertebral abnormality, anal atresia, cardiac abnormality, tracheo-esophageal fistula, renal anomaly, limb defect syndrome with hydrocephalus | Is a | True | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Capra DeMarco syndrome | Is a | True | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Hydrocephalus with endocardial fibroelastosis and cataract syndrome | Is a | True | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Hydrocephalus, cardiac malformation, dense bone syndrome | Is a | True | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Hydrocephalus, costovertebral dysplasia, Sprengel anomaly syndrome | Is a | True | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Hydrocephalus with obesity and hypogonadism syndrome | Is a | True | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Megalencephaly, polymicrogyria, postaxial polydactyly, hydrocephalus syndrome | Is a | True | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Hydrocephalus, tall stature, joint laxity syndrome | Is a | True | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Congenital obstructive hydrocephalus | Is a | True | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Hydrocephalus, blue sclera, nephropathy syndrome | Is a | True | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Hypoplasia of corpus callosum, intellectual disability, adducted thumbs, spasticity, hydrocephalus syndrome | Is a | True | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Hydrocephalus associated with congenital aqueduct stenosis | Is a | True | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Communicating hydrocephalus co-occurrent and due to congenital agenesis of arachnoid villi | Is a | True | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Thoracic dysplasia and hydrocephalus syndrome | Is a | True | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Fetal hydrocephalus | Is a | False | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Port-wine nevi, mega cisterna magna, hydrocephalus syndrome | Is a | True | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Congenital hydrocephalus, low insertion of umbilicus syndrome | Is a | True | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Congenital dilated lateral ventricles of brain | Is a | True | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| [X]Other congenital hydrocephalus | Is a | False | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Congenital hydrocephalus NOS | Is a | False | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  | 
| Other specified congenital hydrocephalus | Is a | False | Congenital hydrocephalus | Inferred relationship | Existential restriction modifier |  |