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1336115002: Pyoderma gangrenosum, acne, hidradenitis suppurativa, ankylosing spondylitis syndrome (disorder)


Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 01-Jun 2024. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
5363457015 Pyoderma gangrenosum, acne, hidradenitis suppurativa, ankylosing spondylitis syndrome (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
5363458013 Pyoderma gangrenosum, acne, hidradenitis suppurativa, ankylosing spondylitis syndrome en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
5363459017 PASS syndrome en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
5363460010 PASS (pyoderma gangrenosum, acne, hidradenitis suppurativa, ankylosing spondylitis) syndrome en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
5363461014 A rare autoinflammatory syndrome with characteristics of a chronic-relapsing course of the combination of pyoderma gangrenosum, acne, hidradenitis suppurativa (which, in addition to axillae and inguinal folds, can be observed on upper and lower limbs, back, and buttocks, among others), and ankylosing spondylitis. Typical age of onset is adolescence to young adulthood, with the different signs and symptoms appearing simultaneously or subsequently. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core


0 descendants.

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Pyoderma gangrenosum, acne, hidradenitis suppurativa, ankylosing spondylitis syndrome (disorder) Is a Acne true Inferred relationship Some
Pyoderma gangrenosum, acne, hidradenitis suppurativa, ankylosing spondylitis syndrome (disorder) Is a Hidradenitis suppurativa pyoderma gangrenosum complex (disorder) true Inferred relationship Some
Pyoderma gangrenosum, acne, hidradenitis suppurativa, ankylosing spondylitis syndrome (disorder) Is a Chronic infectious disease false Inferred relationship Some
Pyoderma gangrenosum, acne, hidradenitis suppurativa, ankylosing spondylitis syndrome (disorder) Is a Chronic dermatitis false Inferred relationship Some
Pyoderma gangrenosum, acne, hidradenitis suppurativa, ankylosing spondylitis syndrome (disorder) Is a Chronic arthropathy false Inferred relationship Some
Pyoderma gangrenosum, acne, hidradenitis suppurativa, ankylosing spondylitis syndrome (disorder) Is a Chronic disease of immune function (disorder) false Inferred relationship Some
Pyoderma gangrenosum, acne, hidradenitis suppurativa, ankylosing spondylitis syndrome (disorder) Is a Chronic disease of immune structure (disorder) false Inferred relationship Some
Pyoderma gangrenosum, acne, hidradenitis suppurativa, ankylosing spondylitis syndrome (disorder) Is a Autoinflammatory disease (disorder) true Inferred relationship Some
Pyoderma gangrenosum, acne, hidradenitis suppurativa, ankylosing spondylitis syndrome (disorder) Is a Ankylosing spondylitis true Inferred relationship Some
Pyoderma gangrenosum, acne, hidradenitis suppurativa, ankylosing spondylitis syndrome (disorder) Clinical course Relapsing course true Inferred relationship Some 6
Pyoderma gangrenosum, acne, hidradenitis suppurativa, ankylosing spondylitis syndrome (disorder) Finding site Skin structure true Inferred relationship Some 1
Pyoderma gangrenosum, acne, hidradenitis suppurativa, ankylosing spondylitis syndrome (disorder) Associated morphology Neutrophilic infiltration true Inferred relationship Some 1
Pyoderma gangrenosum, acne, hidradenitis suppurativa, ankylosing spondylitis syndrome (disorder) Finding site Structure of apocrine sweat gland bearing skin (body structure) true Inferred relationship Some 2
Pyoderma gangrenosum, acne, hidradenitis suppurativa, ankylosing spondylitis syndrome (disorder) Associated morphology Chronic suppurative inflammation true Inferred relationship Some 2
Pyoderma gangrenosum, acne, hidradenitis suppurativa, ankylosing spondylitis syndrome (disorder) Pathological process (attribute) Infectious process (qualifier value) true Inferred relationship Some 2
Pyoderma gangrenosum, acne, hidradenitis suppurativa, ankylosing spondylitis syndrome (disorder) Causative agent Domain Bacteria (organism) true Inferred relationship Some 2
Pyoderma gangrenosum, acne, hidradenitis suppurativa, ankylosing spondylitis syndrome (disorder) Finding site Structure of immune system (body structure) true Inferred relationship Some 3
Pyoderma gangrenosum, acne, hidradenitis suppurativa, ankylosing spondylitis syndrome (disorder) Associated morphology Inflammatory morphology (morphologic abnormality) true Inferred relationship Some 3
Pyoderma gangrenosum, acne, hidradenitis suppurativa, ankylosing spondylitis syndrome (disorder) Pathological process (attribute) Abnormal immune process (qualifier value) true Inferred relationship Some 3
Pyoderma gangrenosum, acne, hidradenitis suppurativa, ankylosing spondylitis syndrome (disorder) Finding site Joint structure of spine true Inferred relationship Some 4
Pyoderma gangrenosum, acne, hidradenitis suppurativa, ankylosing spondylitis syndrome (disorder) Associated morphology Inflammatory morphology (morphologic abnormality) true Inferred relationship Some 4
Pyoderma gangrenosum, acne, hidradenitis suppurativa, ankylosing spondylitis syndrome (disorder) Finding site Pilosebaceous apparatus structure (body structure) true Inferred relationship Some 5
Pyoderma gangrenosum, acne, hidradenitis suppurativa, ankylosing spondylitis syndrome (disorder) Associated morphology Lesion (morphologic abnormality) true Inferred relationship Some 5

Inbound Relationships Type Active Source Characteristic Refinability Group

Reference Sets

Component annotation with string value reference set (foundation metadata concept)

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