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248693006: Chronic idiopathic neutropenia (disorder)


Status: current, Sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jul 2021. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
371202019 Chronic idiopathic neutropenia en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
371204018 Idiopathic agranulocytosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
2528842010 Chronic idiopathic neutropenia (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
4050231000005110 kronisk idiopatisk neutropeni da Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) Danish module (core metadata concept)


1 descendants. Search Descendants:

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Chronic idiopathic neutropenia (disorder) Is a Disorder of phagocytic cell number false Inferred relationship Some
Chronic idiopathic neutropenia (disorder) Is a Neutropenic disorder true Inferred relationship Some
Chronic idiopathic neutropenia (disorder) Finding site Haematopoietic system structure false Inferred relationship Some
Chronic idiopathic neutropenia (disorder) Finding site Structure of immune system (body structure) false Inferred relationship Some
Chronic idiopathic neutropenia (disorder) Finding site Leukocyte false Inferred relationship Some
Chronic idiopathic neutropenia (disorder) Finding site Haematopoietic system structure false Inferred relationship Some
Chronic idiopathic neutropenia (disorder) Associated morphology White blood cell abnormality false Inferred relationship Some
Chronic idiopathic neutropenia (disorder) Has definitional manifestation Immune system finding false Inferred relationship Some
Chronic idiopathic neutropenia (disorder) Has definitional manifestation White blood cell finding false Inferred relationship Some
Chronic idiopathic neutropenia (disorder) Is a Chronic disease of immune function (disorder) true Inferred relationship Some
Chronic idiopathic neutropenia (disorder) Course Chronic false Inferred relationship Some
Chronic idiopathic neutropenia (disorder) Has definitional manifestation Neutropenia (finding) false Inferred relationship Some
Chronic idiopathic neutropenia (disorder) Clinical course Chronic true Inferred relationship Some 2
Chronic idiopathic neutropenia (disorder) Has definitional manifestation Immune system finding false Inferred relationship Some
Chronic idiopathic neutropenia (disorder) Has interpretation Below reference range true Inferred relationship Some 1
Chronic idiopathic neutropenia (disorder) Interprets Neutrophil count true Inferred relationship Some 1
Chronic idiopathic neutropenia (disorder) Pathological process (attribute) Abnormal immune process (qualifier value) true Inferred relationship Some 3
Chronic idiopathic neutropenia (disorder) Is a Neutropenia (finding) false Inferred relationship Some
Chronic idiopathic neutropenia (disorder) Is a Idiopathic disease true Inferred relationship Some

Inbound Relationships Type Active Source Characteristic Refinability Group
A rare acquired immunodeficiency disease with characteristics of adult-onset absolute neutrophil counts less than 1.5 x 10^9/L on at least 3 occasions in a 3 month period that cannot be attributable to drugs or a specific genetic, infectious, inflammatory, autoimmune or malignant cause. Recurrent apthous stomatitis and a history of mild bacterial infections are typically associated. A benign outcome with a low rate of severe infections and no secondary malignancies is observed. Is a True Chronic idiopathic neutropenia (disorder) Inferred relationship Some

This concept is not in any reference sets

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