1290858009: Epithelioid inflammatory myofibroblastic sarcoma (disorder)
- SNOMED CT Concept\Clinical finding (finding)\Disease\Neoplasm and/or hamartoma (disorder)\Neoplastic disease\Neoplastic disease of uncertain behavior\A rare neoplastic lesion of the submucosal stroma, which can develop in any organ, often occurring in the lung, mesentery, omentum and the retroperitoneal region. It is histologically heterogenous, composed of spindle-shaped cells, myofibroblasts and inflammatory cells. It is usually benign, however local invasion, recurrence, malignant transformation with vascular invasion and metastases may occur. The presentation is nonspecific and depends on the organ involved. Some patients may present with paraneoplastic syndrome (fever, malaise, weight loss, thrombocytosis) or symptoms related to compression of adjacent organs, such as bowel obstruction.\Epithelioid inflammatory myofibroblastic sarcoma
Status: current, Sufficiently defined by necessary conditions definition status (core metadata concept). Date: 01-Nov 2023. Module: SNOMED CT core
Descriptions:
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Epithelioid inflammatory myofibroblastic sarcoma |
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A rare neoplastic lesion of the submucosal stroma, which can develop in any organ, often occurring in the lung, mesentery, omentum and the retroperitoneal region. It is histologically heterogenous, composed of spindle-shaped cells, myofibroblasts and inflammatory cells. It is usually benign, however local invasion, recurrence, malignant transformation with vascular invasion and metastases may occur. The presentation is nonspecific and depends on the organ involved. Some patients may present with paraneoplastic syndrome (fever, malaise, weight loss, thrombocytosis) or symptoms related to compression of adjacent organs, such as bowel obstruction. |
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Epithelioid inflammatory myofibroblastic sarcoma |
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Epithelioid inflammatory myofibroblastic sarcoma (morphologic abnormality) |
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This concept is not in any reference sets
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