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773688007: Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder)


Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jan 2019. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
3725773017 CLIPPERS - chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
3725774011 Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
3725775012 Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3725778014 A rare neuroinflammatory disorder with characteristics of brainstem-predominant encephalomyelitis, which typically presents with cerebellar and cranial nerve manifestations (gait ataxia, dysarthria, visual disorders, parasthesia), as well as brainstem, myelopathy and cognitive findings that respond to steroid treatment. Punctate curvilinear post-gadolinium contrast enhancement predominantly in the pons and cerebellum is observed on brain MRI and prominent, perivascular, CD3+ T-cell predominantly lymphocytic inflammation in neuropathology. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core


0 descendants.

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder) Is a Brainstem encephalitis false Inferred relationship Some
Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder) Is a Encephalomyelitis false Inferred relationship Some
Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder) Associated morphology Chronic lymphocytic inflammation true Inferred relationship Some 2
Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder) Finding site Brainstem structure true Inferred relationship Some 2
Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder) Finding site Spinal cord structure true Inferred relationship Some 1
Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder) Associated morphology Chronic lymphocytic inflammation true Inferred relationship Some 1
Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder) Is a Disorder of brain stem (disorder) true Inferred relationship Some
Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder) Is a Inflammatory disorder of head true Inferred relationship Some
Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder) Is a Encephalomyelopathy (disorder) true Inferred relationship Some
Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (disorder) Is a Myelitis true Inferred relationship Some

Inbound Relationships Type Active Source Characteristic Refinability Group

This concept is not in any reference sets

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