721226005: Hughes Stovin syndrome (disorder)

• SNOMED CT Concept\Clinical finding\...
• \General finding of soft tissue\Blood vessel finding\Vascular disorder\Vasculitis\Hughes Stovin syndrome
• \General finding of soft tissue\Disorder of soft tissue\Vascular disorder\Vasculitis\Hughes Stovin syndrome
• \Cardiovascular finding\Cardiovascular disease\Inflammatory disorder of the cardiovascular system\Vasculitis\Hughes Stovin syndrome
• \Cardiovascular finding\Cardiovascular disease\Vascular disorder\Vasculitis\Hughes Stovin syndrome
• \Cardiovascular finding\Blood vessel finding\Vascular disorder\Vasculitis\Hughes Stovin syndrome
• \Disease\Disorder of body system\Inflammation of specific body systems\Inflammatory disorder of the cardiovascular system\Vasculitis\Hughes Stovin syndrome
• \Disease\Disorder of body system\Cardiovascular disease\Inflammatory disorder of the cardiovascular system\Vasculitis\Hughes Stovin syndrome
• \Disease\Disorder of body system\Cardiovascular disease\Vascular disorder\Vasculitis\Hughes Stovin syndrome
• \Disease\Inflammatory disorder\Inflammation of specific body structures or tissue\Inflammation of specific body systems\Inflammatory disorder of the cardiovascular system\Vasculitis\Hughes Stovin syndrome
• \Disease\Inflammatory disorder\Inflammation of specific body structures or tissue\Inflammation of specific body organs\Vasculitis\Hughes Stovin syndrome
• \Disease\Disorder of soft tissue\Vascular disorder\Vasculitis\Hughes Stovin syndrome

Status: current, Primitive. Date: 31-Jan 2017. Module: SNOMED CT core

Descriptions:

Id	Description	Lang	Type	Status	Case?	Module
3324673014	Hughes Stovin syndrome (disorder)	en	Fully specified name	Active	Case sensitive	SNOMED CT core
3324676018	Hughes Stovin syndrome	en	Synonym	Active	Case sensitive	SNOMED CT core
3324678017	A life-threatening disorder, believed to be a cardiovascular clinical variant manifestation of Behcet disease, with the association of multiple pulmonary artery aneurysms and peripheral venous thrombosis. Prevalence is unknown but fewer than 30 cases have been reported in the literature since its first description in 1959 by Hughes and Stovin. Patients (mostly men aged 12-40 years) generally present with the nonspecific signs of pulmonary artery aneurysms, following a history of peripheral venous thrombosis. Other associated signs may include fever and intracranial hypertension. Aneurysms can occur anywhere in the systemic circulation. Recurrent phlebitis also commonly involves the large vessels, resulting in thrombus formation. In general, there is a predisposition for thrombus formation affecting the peripheral veins. It is assumed the disease is a form of vasculitis following a similar mechanism of pathogenesis to that thought to be involved in Behcet disease.	en	Definition	Active	Case sensitive	SNOMED CT core

Expanded Value Set

Reference Sets

Australian emergency department reference set

Clinical finding foundation reference set

Cardiovascular finding reference set

Problem/Diagnosis reference set

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