Status: current, Defined. Date: 31-Jul 2018. Module: SNOMED CT core
Descriptions:
Id | Description | Lang | Type | Status | Case? | Module |
1784908015 | Acquired von Willebrand syndrome | en | Synonym | Active | Initial character case insensitive | SNOMED CT core |
1784909011 | Acquired von Willebrand disease | en | Synonym | Active | Initial character case insensitive | SNOMED CT core |
351278015 | Acquired von Willebrand's disease | en | Synonym | Active | Initial character case insensitive | SNOMED CT core |
5156395019 | Acquired von Willebrand disease (disorder) | en | Fully specified name | Active | Initial character case insensitive | SNOMED CT core |
5156397010 | Acquired von Willebrand disease (VWD) is a rare bleeding disorder marked by the same biological anomalies as those seen in hereditary von Willebrand disease (VWD) but which occurs in association with another underlying pathology, generally in elderly patients without any personal or family history of bleeding anomalies. There are three principle pathogenic mechanisms described which are firstly the presence of autoantibodies (inhibiting or noninhibiting) that form immune complexes with the von Willebrand factor (VWF) leading to rapid clearance of VWF from the circulation. Secondly, absorption of VWF onto malignant cell clones and thirdly the increased proteolysis of high molecular weight VWF multimers under abnormal blood conditions caused by cardiovascular malformations (such as aortic valve stenosis). | en | Definition | Active | Case sensitive | SNOMED CT core |
Outbound Relationships | Type | Target | Active | Characteristic | Refinability | Group | Values |
Acquired von Willebrand's disease | Has interpretation | Abnormal | true | Inferred relationship | Some | 2 | |
Acquired von Willebrand's disease | Interprets | Haemostatic function | true | Inferred relationship | Some | 2 | |
Acquired von Willebrand's disease | Finding site | Body system structure | false | Inferred relationship | Some | ||
Acquired von Willebrand's disease | Has definitional manifestation | Haemostatic system finding | false | Inferred relationship | Some | ||
Acquired von Willebrand's disease | Is a | von Willebrand disorder | true | Inferred relationship | Some | ||
Acquired von Willebrand's disease | Finding site | Entire haematological system | false | Inferred relationship | Some | ||
Acquired von Willebrand's disease | Occurrence | Period of life between birth and death | true | Inferred relationship | Some | 1 | |
Acquired von Willebrand's disease | Is a | Acquired coagulation disorder | true | Inferred relationship | Some |
Inbound Relationships | Type | Active | Source | Characteristic | Refinability | Group |
von Willebrand factor inhibitor disorder | Is a | True | Acquired von Willebrand's disease | Inferred relationship | Some |
Reference Sets
Australian emergency department reference set
Clinical finding foundation reference set
Problem/Diagnosis reference set