Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jul 2018. Module: SNOMED CT core
Descriptions:
Id | Description | Lang | Type | Status | Case? | Module |
1008751000172110 | spectre syndrome de Stevens-Johnson/nécrolyse épidermique toxique | fr | Synonym (core metadata concept) | Active | Entire term case sensitive (core metadata concept) | SNOMED CT Common French translation module (core metadata concept) |
3687582015 | Stevens-Johnson syndrome, toxic epidermal necrolysis spectrum (disorder) | en | Fully specified name | Active | Entire term case sensitive (core metadata concept) | SNOMED CT core |
3687583013 | Stevens-Johnson syndrome, toxic epidermal necrolysis spectrum | en | Synonym (core metadata concept) | Active | Entire term case sensitive (core metadata concept) | SNOMED CT core |
3687587014 | Toxic epidermolysis | en | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | SNOMED CT core |
769171000241119 | spectre syndrome de Stevens-Johnson/nécrolyse épidermique toxique (trouble) | fr | Fully specified name | Active | Entire term case sensitive (core metadata concept) | SNOMED CT Common French translation module (core metadata concept) |
902601000172111 | epidermolyse toxique | fr | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | SNOMED CT Common French translation module (core metadata concept) |
3687603019 | An acute and severe skin disease with clinical and histological features of destruction and detachment of the skin epithelium and mucous membranes. Onset may occur at any age, but the risk increases after 40 years. Three subforms have been described according to the percentage of the body surface area affected: Stevens-Johnson syndrome (less than 10%), Lyell syndrome (greater than 30%) and an intermediate form (10-29%). The initial manifestations are nonspecific: a seemingly banal rash, fever, and a burning sensation involving the eyes, mouth and genitalia. The rash rapidly progresses to become vesicular and bullous on the face and body. High fever is a constant feature. Two thirds of cases are triggered by a drug allergy. In rare cases, the disease is associated with infections or bone marrow transplantation. The remaining 25-30% of cases are classed as idiopathic. The prognosis for patients with extensive forms is poor. | en | Definition | Active | Entire term case sensitive (core metadata concept) | SNOMED CT core |
Outbound Relationships | Type | Target | Active | Characteristic | Refinability | Group | Values |
spectre syndrome de Stevens-Johnson/nécrolyse épidermique toxique | est un(e) (attribut) | Acute eruption of skin (disorder) | true | Inferred relationship | Some | ||
spectre syndrome de Stevens-Johnson/nécrolyse épidermique toxique | est un(e) (attribut) | Erythroderma (disorder) | false | Inferred relationship | Some | ||
spectre syndrome de Stevens-Johnson/nécrolyse épidermique toxique | localisation d'une constatation (attribut) | structure de la peau | true | Inferred relationship | Some | 2 | |
spectre syndrome de Stevens-Johnson/nécrolyse épidermique toxique | évolution clinique (attribut) | Sudden onset AND/OR short duration (qualifier value) | true | Inferred relationship | Some | 4 | |
spectre syndrome de Stevens-Johnson/nécrolyse épidermique toxique | est un(e) (attribut) | Skin necrosis | true | Inferred relationship | Some | ||
spectre syndrome de Stevens-Johnson/nécrolyse épidermique toxique | est un(e) (attribut) | affection cutanée aiguë | false | Inferred relationship | Some | ||
spectre syndrome de Stevens-Johnson/nécrolyse épidermique toxique | est un(e) (attribut) | Acute erythematous eruption of skin (finding) | true | Inferred relationship | Some | ||
spectre syndrome de Stevens-Johnson/nécrolyse épidermique toxique | est un(e) (attribut) | Erythematous condition | false | Inferred relationship | Some | ||
spectre syndrome de Stevens-Johnson/nécrolyse épidermique toxique | morphologie associée (attribut) | Necrosis | true | Inferred relationship | Some | 2 | |
spectre syndrome de Stevens-Johnson/nécrolyse épidermique toxique | morphologie associée (attribut) | érythème (anomalie morphologique) | true | Inferred relationship | Some | 1 | |
spectre syndrome de Stevens-Johnson/nécrolyse épidermique toxique | localisation d'une constatation (attribut) | structure de la peau | true | Inferred relationship | Some | 1 | |
spectre syndrome de Stevens-Johnson/nécrolyse épidermique toxique | morphologie associée (attribut) | Separation | true | Inferred relationship | Some | 3 | |
spectre syndrome de Stevens-Johnson/nécrolyse épidermique toxique | localisation d'une constatation (attribut) | peau et/ou muqueuse | true | Inferred relationship | Some | 3 |
Inbound Relationships | Type | Active | Source | Characteristic | Refinability | Group |
syndrome de Lyell (trouble) | est un(e) (attribut) | True | spectre syndrome de Stevens-Johnson/nécrolyse épidermique toxique | Inferred relationship | Some | |
Stevens Johnson syndrome AND toxic epidermal necrolysis overlap | est un(e) (attribut) | True | spectre syndrome de Stevens-Johnson/nécrolyse épidermique toxique | Inferred relationship | Some | |
Stevens-Johnson syndrome | est un(e) (attribut) | True | spectre syndrome de Stevens-Johnson/nécrolyse épidermique toxique | Inferred relationship | Some |
This concept is not in any reference sets