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20484008: Prion disease (disorder)


Status: current, Sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jan 2002. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
194881000077117 maladie à prion fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Common French translation module (core metadata concept)
34472014 Prion disease en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
4551687011 Transmissible spongiform encephalopathy en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
471661000077115 maladie à prion (trouble) fr Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT Common French translation module (core metadata concept)
749644017 Prion disease (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core


19 descendants. Search Descendants:

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
maladie à prion est un(e) (attribut) maladie infectieuse de l'encéphale true Inferred relationship Some
maladie à prion est un(e) (attribut) Congenital anomaly of head false Inferred relationship Some
maladie à prion est un(e) (attribut) Spongy degeneration of central nervous system false Inferred relationship Some
maladie à prion est un(e) (attribut) Non-specific brain syndrome false Inferred relationship Some
maladie à prion survenue (attribut) congénital false Inferred relationship Some
maladie à prion localisation d'une constatation (attribut) structure du tissu encéphalique false Inferred relationship Some 1
maladie à prion morphologie associée (attribut) Spongy degeneration false Inferred relationship Some 1
maladie à prion est un(e) (attribut) dégénérescence cérébrale principalement présente dans la démence false Inferred relationship Some
maladie à prion est un(e) (attribut) maladie infectieuse false Inferred relationship Some
maladie à prion est un(e) (attribut) Congenital infectious disease false Inferred relationship Some
maladie à prion morphologie associée (attribut) dégénérescence false Inferred relationship Some 2
maladie à prion localisation d'une constatation (attribut) structure du cerveau false Inferred relationship Some 2
maladie à prion est défini par la manifestation de (attribut) démence false Inferred relationship Some
maladie à prion morphologie associée (attribut) Spongy degeneration false Inferred relationship Some 1
maladie à prion localisation d'une constatation (attribut) structure du tissu encéphalique false Inferred relationship Some 1
maladie à prion morphologie associée (attribut) dégénérescence false Inferred relationship Some 2
maladie à prion localisation d'une constatation (attribut) structure du cerveau false Inferred relationship Some 2
maladie à prion Pathological process (attribute) Infectious process (qualifier value) false Inferred relationship Some
maladie à prion est un(e) (attribut) maladie infectieuse false Inferred relationship Some
maladie à prion est un(e) (attribut) trouble infectieux de la tête false Inferred relationship Some
maladie à prion Causative agent Prion true Inferred relationship Some 3
maladie à prion morphologie associée (attribut) Spongy degeneration true Inferred relationship Some 3
maladie à prion localisation d'une constatation (attribut) structure du tissu encéphalique true Inferred relationship Some 3
maladie à prion Pathological process (attribute) Infectious process (qualifier value) true Inferred relationship Some 3
maladie à prion est un(e) (attribut) Degenerative brain disorder true Inferred relationship Some
maladie à prion morphologie associée (attribut) dégénérescence false Inferred relationship Some 1
maladie à prion localisation d'une constatation (attribut) Structure of central nervous system (body structure) false Inferred relationship Some 1
maladie à prion processus pathologique maladie infectieuse false Inferred relationship Some
maladie à prion localisation d'une constatation (attribut) Structure of telencephalon false Inferred relationship Some
maladie à prion Causative agent Prion false Inferred relationship Some

Inbound Relationships Type Active Source Characteristic Refinability Group
Tic disorder due to prion disease Due to True maladie à prion Inferred relationship Some 2
Parkinsonism due to prion disease (disorder) Due to True maladie à prion Inferred relationship Some 2
Chronic wasting disease of captive mule deer AND/OR elk est un(e) (attribut) False maladie à prion Inferred relationship Some
Bovine spongiform encephalopathy (disorder) est un(e) (attribut) False maladie à prion Inferred relationship Some
Gerstmann-Straussler-Scheinker syndrome est un(e) (attribut) True maladie à prion Inferred relationship Some
Transmissible mink encephalopathy est un(e) (attribut) False maladie à prion Inferred relationship Some
Bovine spongiform encephalopathy (disorder) est un(e) (attribut) False maladie à prion Inferred relationship Some
maladie de Creutzfeldt-Jakob est un(e) (attribut) True maladie à prion Inferred relationship Some
Fatal familial insomnia est un(e) (attribut) True maladie à prion Inferred relationship Some
Kuru est un(e) (attribut) False maladie à prion Inferred relationship Some
Prion disease associated with AIDS est un(e) (attribut) False maladie à prion Inferred relationship Some
Progressive subcortical gliosis est un(e) (attribut) True maladie à prion Inferred relationship Some
dégénérescence cérébrale causée par l'encéphalopathie spongiforme subaiguë est un(e) (attribut) False maladie à prion Inferred relationship Some
[X]Dementia in Creutzfeldt-Jakob disease est un(e) (attribut) False maladie à prion Inferred relationship Some
encéphalopathie spongiforme est un(e) (attribut) True maladie à prion Inferred relationship Some
variante de la maladie de Creutzfeldt-Jakob est un(e) (attribut) True maladie à prion Inferred relationship Some
Familial Alzheimer-like prion disease (disorder) est un(e) (attribut) True maladie à prion Inferred relationship Some
Variably protease sensitive prionopathy (disorder) est un(e) (attribut) True maladie à prion Inferred relationship Some
Acquired prion disease (disorder) est un(e) (attribut) True maladie à prion Inferred relationship Some
Prion protein systemic amyloidosis (disorder) est un(e) (attribut) True maladie à prion Inferred relationship Some
Dementia due to prion disease Due to True maladie à prion Inferred relationship Some 2

Reference Sets

Client's clinical problems, conditions, diagnoses, symptoms, findings, complaints reference set (foundation metadata concept)

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