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1187615007: Thrombocytopenia, anasarca, fever, renal insufficiency, organomegaly syndrome (disorder)


Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jan 2022. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
4674359014 Thrombocytopenia, anasarca, fever, renal insufficiency, organomegaly syndrome (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
4674360016 TAFRO syndrome en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
4674361017 TAFRO (thrombocytopenia, anasarca, fever, renal insufficiency, organomegaly) syndrome en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
4674362012 Thrombocytopenia, anasarca, fever, renal insufficiency, organomegaly syndrome en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
4674363019 A rare systemic disease characterized by acute or subacute onset of thrombocytopenia, anasarca (edema, pleural effusion, ascites) and systemic inflammation (fever and/or elevated C-reactive protein). Minor diagnostic categories are Castleman disease-like features on lymph node biopsy, reticulin myelofibrosis and/or increased number of megakaryocytes in bone marrow, progressive renal insufficiency and mild organomegaly including hepatosplenomegaly and lymphadenopathy. Most patients show elevated levels of serum alkaline phosphatase while marked polyclonal hypergammopathy is rare. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
4674364013 A rare systemic disease characterised by acute or subacute onset of thrombocytopenia, anasarca (oedema, pleural effusion, ascites) and systemic inflammation (fever and/or elevated C-reactive protein). Minor diagnostic categories are Castleman disease-like features on lymph node biopsy, reticulin myelofibrosis and/or increased number of megakaryocytes in bone marrow, progressive renal insufficiency and mild organomegaly including hepatosplenomegaly and lymphadenopathy. Most patients show elevated levels of serum alkaline phosphatase while marked polyclonal hypergammopathy is rare. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core


0 descendants.

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Thrombocytopenia, anasarca, fever, renal insufficiency, organomegaly syndrome (disorder) est un(e) (attribut) Disorder characterized by edema true Inferred relationship Some
Thrombocytopenia, anasarca, fever, renal insufficiency, organomegaly syndrome (disorder) est un(e) (attribut) Inflammatory disorder true Inferred relationship Some
Thrombocytopenia, anasarca, fever, renal insufficiency, organomegaly syndrome (disorder) est un(e) (attribut) trouble thrombocytopénique true Inferred relationship Some
Thrombocytopenia, anasarca, fever, renal insufficiency, organomegaly syndrome (disorder) est un(e) (attribut) Fever true Inferred relationship Some
Thrombocytopenia, anasarca, fever, renal insufficiency, organomegaly syndrome (disorder) est un(e) (attribut) anasarque true Inferred relationship Some
Thrombocytopenia, anasarca, fever, renal insufficiency, organomegaly syndrome (disorder) est un(e) (attribut) maladie systémique true Inferred relationship Some
Thrombocytopenia, anasarca, fever, renal insufficiency, organomegaly syndrome (disorder) morphologie associée (attribut) Anasarca true Inferred relationship Some 3
Thrombocytopenia, anasarca, fever, renal insufficiency, organomegaly syndrome (disorder) morphologie associée (attribut) Inflammatory morphology (morphologic abnormality) true Inferred relationship Some 4
Thrombocytopenia, anasarca, fever, renal insufficiency, organomegaly syndrome (disorder) interprète (attribut) Hemostatic function (observable entity) true Inferred relationship Some 1
Thrombocytopenia, anasarca, fever, renal insufficiency, organomegaly syndrome (disorder) a pour interprétation (attribut) anormal true Inferred relationship Some 1
Thrombocytopenia, anasarca, fever, renal insufficiency, organomegaly syndrome (disorder) interprète (attribut) Platelet count true Inferred relationship Some 2
Thrombocytopenia, anasarca, fever, renal insufficiency, organomegaly syndrome (disorder) a pour interprétation (attribut) au-dessous de l'étendue de référence true Inferred relationship Some 2
Thrombocytopenia, anasarca, fever, renal insufficiency, organomegaly syndrome (disorder) interprète (attribut) Body temperature (observable entity) true Inferred relationship Some 5
Thrombocytopenia, anasarca, fever, renal insufficiency, organomegaly syndrome (disorder) a pour interprétation (attribut) au-dessus de l'étendue de référence true Inferred relationship Some 5
Thrombocytopenia, anasarca, fever, renal insufficiency, organomegaly syndrome (disorder) est un(e) (attribut) trouble caractérisé par de la fièvre true Inferred relationship Some

Inbound Relationships Type Active Source Characteristic Refinability Group

This concept is not in any reference sets

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