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1169361002: Limbic encephalitis with neurexin-3 antibodies (disorder)


Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 30-Sep 2021. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
4607805016 Limbic encephalitis with neurexin-3 antibodies (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
4607807012 Limbic encephalitis with neurexin-3 antibodies en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
4607806015 A rare non-paraneoplastic limbic encephalitis with characteristics of severe but potentially treatable autoimmune encephalitis associated with autoantibodies against neurexin-3alpha. Patients present with prodromal fever, headache, or gastrointestinal symptoms, followed by rapid progression to confusion, seizures, and decreased level of consciousness. Mild orofacial dyskinesia, as well as life-threatening complications like central hypoventilation requiring respiratory support may develop in some patients. en Definition Inactive Entire term case sensitive (core metadata concept) SNOMED CT core
13984391000172112 encéphalite limbique avec anticorps antineurexine 3 fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) Belgian module (core metadata concept)
7173521000172119 limbische hersenontsteking met neurexine-3-antistoffen nl Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) Belgian module (core metadata concept)
7173531000172116 limbische encefalitis met neurexine-3-antilichamen nl Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) Belgian module (core metadata concept)


0 descendants.

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Limbic encephalitis with neurexin-3 antibodies (disorder) Is a Limbic encephalitis true Inferred relationship Some
Limbic encephalitis with neurexin-3 antibodies (disorder) Finding site Limbic system structure true Inferred relationship Some 1
Limbic encephalitis with neurexin-3 antibodies (disorder) Associated morphology Inflammatory morphology (morphologic abnormality) true Inferred relationship Some 1
Limbic encephalitis with neurexin-3 antibodies (disorder) Is a Autoimmune encephalitis true Inferred relationship Some
Limbic encephalitis with neurexin-3 antibodies (disorder) Pathological process (attribute) Autoimmune process true Inferred relationship Some 1

Inbound Relationships Type Active Source Characteristic Refinability Group

Reference Sets

GB English

US English

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