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829971006: niet-amyloïde monoklonale immuunglobulinestapelingsziekte (aandoening)


Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jul 2020. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
3880130012 Non-amyloid monoclonal immunoglobulin deposition disease (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
3880131011 Non-amyloid monoclonal immunoglobulin deposition disease en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3880132016 Randall disease en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
3880133014 Non-amyloid MIDD (monoclonal immunoglobulin deposition disease) en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
10954971000146114 niet-amyloïde MIDD nl Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT Netherlands NRC maintained module (core metadata concept)
11165191000146113 niet-amyloïde monoklonale immuunglobulinestapelingsziekte (aandoening) nl Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT Netherlands NRC maintained module (core metadata concept)
11165201000146110 niet-amyloïde monoklonale immuunglobulinestapelingsziekte nl Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Netherlands NRC maintained module (core metadata concept)
13345651000146119 niet-amyloïde 'monoclonal immunoglobulin deposition disease' nl Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Netherlands NRC maintained module (core metadata concept)
3880134015 A rare secondary glomerular disease characterized by proteinuria, dysproteinemia, nephrotic syndrome, and nodular glomerulopathy leading to renal failure, with or without extra-renal manifestations. The renal biopsy shows typical deposits of monoclonal immunoglobulins that do not show a fibrillar organization and are negative for Congo red staining. Associated signs and symptoms depend on the involvement of other organs, liver, heart, nerve fibers, gastrointestinal tract or skin. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
3880135019 A rare secondary glomerular disease characterised by proteinuria, dysproteinaemia, nephrotic syndrome, and nodular glomerulopathy leading to renal failure, with or without extra-renal manifestations. The renal biopsy shows typical deposits of monoclonal immunoglobulins that do not show a fibrillar organisation and are negative for Congo red staining. Associated signs and symptoms depend on the involvement of other organs, liver, heart, nerve fibres, gastrointestinal tract or skin. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core


2 descendants. Search Descendants:

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Non-amyloid monoclonal immunoglobulin deposition disease (disorder) Is a Glomerular disease true Inferred relationship Some
Non-amyloid monoclonal immunoglobulin deposition disease (disorder) Finding site Glomerulus structure true Inferred relationship Some 1
Non-amyloid monoclonal immunoglobulin deposition disease (disorder) Interprets Serum globulin measurement true Inferred relationship Some 2
Non-amyloid monoclonal immunoglobulin deposition disease (disorder) Has interpretation Above reference range true Inferred relationship Some 2
Non-amyloid monoclonal immunoglobulin deposition disease (disorder) Interprets Immunoglobulin measurement true Inferred relationship Some 3
Non-amyloid monoclonal immunoglobulin deposition disease (disorder) Has interpretation Above reference range true Inferred relationship Some 3
Non-amyloid monoclonal immunoglobulin deposition disease (disorder) Has interpretation Present false Inferred relationship Some 4
Non-amyloid monoclonal immunoglobulin deposition disease (disorder) Interprets Paraprotein measurement true Inferred relationship Some 4
Non-amyloid monoclonal immunoglobulin deposition disease (disorder) Is a Plasma cell neoplasm (disorder) true Inferred relationship Some
Non-amyloid monoclonal immunoglobulin deposition disease (disorder) Is a Neoplasm of uncertain behavior of kidney true Inferred relationship Some
Non-amyloid monoclonal immunoglobulin deposition disease (disorder) Is a Hematologic neoplasm of uncertain behavior true Inferred relationship Some
Non-amyloid monoclonal immunoglobulin deposition disease (disorder) Is a Monoclonal gammopathy (clinical) true Inferred relationship Some
Non-amyloid monoclonal immunoglobulin deposition disease (disorder) Pathological process (attribute) Abnormal immune process (qualifier value) true Inferred relationship Some 1
Non-amyloid monoclonal immunoglobulin deposition disease (disorder) Associated morphology Immunoglobulin deposition disease true Inferred relationship Some 1
Non-amyloid monoclonal immunoglobulin deposition disease (disorder) Is a Neoplasm of parenchyma of kidney (disorder) true Inferred relationship Some
Non-amyloid monoclonal immunoglobulin deposition disease (disorder) Has interpretation Detected true Inferred relationship Some 4

Inbound Relationships Type Active Source Characteristic Refinability Group
Heavy chain deposition disease Is a True Non-amyloid monoclonal immunoglobulin deposition disease (disorder) Inferred relationship Some

This concept is not in any reference sets

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