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715863001: immuungemedieerde necrotiserende myopathie (aandoening)


Status: current, Sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jul 2019. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
3303966017 Autoimmune necrotizing myopathy (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
3303967014 Autoimmune necrotizing myopathy en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3303968016 Autoimmune necrotising myopathy en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3303969012 Immune mediated necrotizing myopathy en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3303970013 Immune mediated necrotising myopathy en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
5624221000146113 auto-immune necrotiserende myopathie nl Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Netherlands NRC maintained module (core metadata concept)
5624231000146110 INM nl Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Netherlands NRC maintained module (core metadata concept)
5624261000146118 IMNM nl Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Netherlands NRC maintained module (core metadata concept)
6716051000146115 immuungemedieerde necrotiserende myopathie (aandoening) nl Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT Netherlands NRC maintained module (core metadata concept)
6716061000146117 immuungemedieerde necrotiserende myopathie nl Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Netherlands NRC maintained module (core metadata concept)
3303971012 A rare form of idiopathic inflammatory myopathy with clinical manifestation of acute or subacute proximal muscle weakness and histopathological features of myocyte necrosis and regeneration without significant inflammation. The main presenting feature is subacute severe symmetrical proximal myopathy with a markedly elevated creatine kinase level. The course is often severe but may be self-limiting and recovery may occur within weeks to months of discontinuing the causative agent, if identified. The disease is thought to be related to an immune response possibly triggered by drug therapy, connective tissue diseases, or cancer. The exact mechanism underling the disorder is not known but some autoantibodies appear to be a likely cause. Malignancy may be involved. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core


0 descendants.

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Autoimmune necrotizing myopathy (disorder) Is a Autoimmune disease false Inferred relationship Some
Autoimmune necrotizing myopathy (disorder) Is a Inflammation of specific body organs false Inferred relationship Some
Autoimmune necrotizing myopathy (disorder) Is a Necrosis of anatomical site false Inferred relationship Some
Autoimmune necrotizing myopathy (disorder) Is a Idiopathic inflammatory myopathy (disorder) true Inferred relationship Some
Autoimmune necrotizing myopathy (disorder) Associated morphology Necrotizing inflammation true Inferred relationship Some 1
Autoimmune necrotizing myopathy (disorder) Finding site Skeletal and/or smooth muscle structure (body structure) false Inferred relationship Some 1
Autoimmune necrotizing myopathy (disorder) Pathological process (attribute) Autoimmune process true Inferred relationship Some 1
Autoimmune necrotizing myopathy (disorder) Is a Autoimmune inflammation of skeletal muscle (disorder) true Inferred relationship Some
Autoimmune necrotizing myopathy (disorder) Finding site Skeletal muscle structure true Inferred relationship Some 1
Autoimmune necrotizing myopathy (disorder) Is a Soft tissue lesion false Inferred relationship Some
Autoimmune necrotizing myopathy (disorder) Is a Injury of musculoskeletal system true Inferred relationship Some
Autoimmune necrotizing myopathy (disorder) Is a Injury of muscle true Inferred relationship Some
Autoimmune necrotizing myopathy (disorder) Is a Soft tissue injury false Inferred relationship Some
Autoimmune necrotizing myopathy (disorder) Is a Lesion of skeletal muscle (disorder) true Inferred relationship Some
Autoimmune necrotizing myopathy (disorder) Is a auto-inflammatoire aandoening (aandoening) false Inferred relationship Some
Autoimmune necrotizing myopathy (disorder) Is a Necrosis of soft tissues (disorder) true Inferred relationship Some

Inbound Relationships Type Active Source Characteristic Refinability Group

Reference Sets

Dutch pathology simple reference set (foundation metadata concept)

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